Esophageal Atresia of Kluth Type-13: Management of a Rare Variant (Case Report)

Maitreyee Save, Aditi Dalvi, Shahaji Deshmukh, Abhaya Gupta, Paras Kothari

Department of Pediatric Surgery, Lokmanya Tilak Municipal Medical College, Sion, Mumbai 400022, India.

Keywords

Congenital malformation

Esophageal atresia

Neonatal pathology

Abbreviations

EA - Esophageal atresia

POD - post-operative day

TEF - Tracheo-esophageal fistula

Abstract

A full-term low birth-weight female newborn presented with clinical features of esophageal atresia. Investigations revealed Kluth type-13, an extremely rare varient of esophageal atresia without fistula, in which the upper pouch is long and ends blindly just above the diaphragm near the gastro-esophageal junction. She was managed with esophagostomy and feeding gastrostomy in the neonatal period, followed by gastric tube esophagoplasty at 2 years of age. At 18 months of follow-up she is thriving well and asymptomatic.